Diseases [C] » Eye Diseases [C11] » Eye Abnormalities » Persistent Hyperplastic Primary Vitreous
Diseases [C] » Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] » Congenital Abnormalities » Eye Abnormalities » Persistent Hyperplastic Primary Vitreous
Description
A developmental ocular anomaly in which the primary VITREOUS BODY and its surrounding hyaloid vasculature failed to regress. It is usually unilateral and characterized by CATARACT; MICROPHTHALMOS (small eyeballs), and retrolenticular fibrovascular tissue. (from Yanoff: Ophthalmology, 2nd ed.) MeSH
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