1-Pyrroline-5-Carboxylate Dehydrogenase D050842

Chemicals and Drugs [D] » Enzymes and Coenzymes [D08] » Enzymes » Oxidoreductases » Oxidoreductases Acting on CH-NH Group Donors » 1-Pyrroline-5-Carboxylate Dehydrogenase

Description

An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.   MeSH

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