Glycine Dehydrogenase (Decarboxylating) D050841

Chemicals and Drugs [D] » Enzymes and Coenzymes [D08] » Enzymes » Oxidoreductases » Oxidoreductases Acting on CH-NH2 Group Donors » Amino Acid Oxidoreductases » Glycine Decarboxylase Complex » Glycine Dehydrogenase (Decarboxylating)

Chemicals and Drugs [D] » Macromolecular Substances [D05] » Multiprotein Complexes » Multienzyme Complexes » Glycine Decarboxylase Complex » Glycine Dehydrogenase (Decarboxylating)

Chemicals and Drugs [D] » Enzymes and Coenzymes [D08] » Enzymes » Multienzyme Complexes » Glycine Decarboxylase Complex » Glycine Dehydrogenase (Decarboxylating)

Description

A PYRIDOXAL PHOSPHATE dependent enzyme that catalyzes the decarboxylation of GLYCINE with the transfer of an aminomethyl group to the LIPOIC ACID moiety of the GLYCINE DECARBOXYLASE COMPLEX H-PROTEIN. Defects in P-protein are the cause of non-ketotic hyperglycinemia. It is one of four subunits of the glycine decarboxylase complex.   MeSH

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