Incontinentia Pigmenti D007184

Related MeSH Hierarchy (6)

Diseases [C] » Skin and Connective Tissue Diseases [C17] » Skin Diseases » Pigmentation Disorders » Incontinentia Pigmenti

Diseases [C] » Skin and Connective Tissue Diseases [C17] » Skin Diseases » Skin Abnormalities » Incontinentia Pigmenti

Diseases [C] » Skin and Connective Tissue Diseases [C17] » Skin Diseases » Skin Diseases, Genetic » Incontinentia Pigmenti

Description

A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.   MeSH

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