Diseases [C] » Respiratory Tract Diseases [C08] » Respiratory System Abnormalities » Bronchopulmonary Sequestration
Diseases [C] » Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] » Congenital Abnormalities » Respiratory System Abnormalities » Bronchopulmonary Sequestration
Description
A developmental anomaly in which a mass of nonfunctioning lung tissue lacks normal connection with the tracheobroncheal tree and receives an anomalous blood supply originating from the descending thoracic or abdominal aorta. The mass may be extralobar, i.e., completely separated from normally connected lung, or intralobar, i.e., partly surrounded by normal lung. MeSH
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