Related MeSH Hierarchy (5)
Diseases [C] » Hemic and Lymphatic Diseases [C15] » Hematologic Diseases » Blood Coagulation Disorders » Purpura » Purpura, Thrombocytopenic » Purpura, Thrombotic Thrombocytopenic
Diseases [C] » Hemic and Lymphatic Diseases [C15] » Hematologic Diseases » Blood Platelet Disorders » Thrombocytopenia » Thrombotic Microangiopathies » Purpura, Thrombocytopenic » Purpura, Thrombotic Thrombocytopenic
Diseases [C] » Hemic and Lymphatic Diseases [C15] » Hematologic Diseases » Thrombophilia » Purpura, Thrombotic Thrombocytopenic
Diseases [C] » Pathological Conditions, Signs and Symptoms [C23] » Pathologic Processes » Hemorrhage » Purpura » Purpura, Thrombocytopenic » Purpura, Thrombotic Thrombocytopenic
Diseases [C] » Pathological Conditions, Signs and Symptoms [C23] » Signs and Symptoms » Skin Manifestations » Purpura » Purpura, Thrombocytopenic » Purpura, Thrombotic Thrombocytopenic
Description
An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases. MeSH
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Approved Indicated Drugs (1)
Phase 4 Indicated Drugs (1)
Phase 2 Indicated Drugs (4)
Organization Involved with Phase 4 Indications (1)
Organization Involved with Phase 3 Indications (25)
Organization Involved with Phase 2 Indications (16)
Organization Involved with Phase 1 Indications (2)
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UMLS Data
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