Lymphangiosarcoma D008204

Diseases [C] » Neoplasms [C04] » Neoplasms by Histologic Type » Lymphatic Vessel Tumors » Lymphangiosarcoma

Diseases [C] » Neoplasms [C04] » Neoplasms by Histologic Type » Neoplasms, Connective and Soft Tissue » Sarcoma » Lymphangiosarcoma

Description

A malignant tumor originating from the endothelial cells of lymphatic vessels. Most lymphangiosarcomas arise in an arm secondary to radical mastectomy but they sometimes complicate idiopathic lymphedema. The lymphedema has usually been present for 6 to 10 years before malignant changes develop. (From Dorland, 27th ed; Holland et al., Cancer Medicine, 3d ed, p1866)   MeSH

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Phase 2 Indicated Drugs (2)


Organization Involved with Phase 2 Indications (1)

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UMLS Data


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