Related MeSH Hierarchy (6)
Diseases [C] » Cardiovascular Diseases [C14] » Cardiovascular Abnormalities » Heart Defects, Congenital » Isolated Noncompaction of the Ventricular Myocardium
Diseases [C] » Cardiovascular Diseases [C14] » Heart Diseases » Cardiomyopathies » Endocardial Fibroelastosis » Isolated Noncompaction of the Ventricular Myocardium
Diseases [C] » Cardiovascular Diseases [C14] » Heart Diseases » Heart Defects, Congenital » Isolated Noncompaction of the Ventricular Myocardium
Diseases [C] » Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] » Congenital Abnormalities » Abnormalities, Multiple » Isolated Noncompaction of the Ventricular Myocardium
Diseases [C] » Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] » Congenital Abnormalities » Cardiovascular Abnormalities » Heart Defects, Congenital » Isolated Noncompaction of the Ventricular Myocardium
Diseases [C] » Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] » Genetic Diseases, Inborn » Genetic Diseases, X-Linked » Isolated Noncompaction of the Ventricular Myocardium
Description
Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen. MeSH
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