Perivascular Epithelioid Cell Neoplasms D054973

Diseases [C] » Neoplasms [C04] » Neoplasms by Histologic Type » Neoplasms, Connective and Soft Tissue » Perivascular Epithelioid Cell Neoplasms

Description

A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. These cells do not have a normal anatomic homolog. (From Fletcher CDM, et. al., World Health Organization Classification of Tumors: Pathology and Genetics of Tumors of Soft Tissue and Bone, 2002).   MeSH

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Subtype Terms (2)

Angiomyolipoma
2 approved drugs

Lymphangioleiomyomatosis
21 drugs (18 approved, 3 experimental)


Phase 2 Indicated Drugs (3)


Organization Involved with Phase 2 Indications (2)

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UMLS Data


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