Malignant Atrophic Papulosis D054853

Diseases [C] » Cardiovascular Diseases [C14] » Vascular Diseases » Arterial Occlusive Diseases » Malignant Atrophic Papulosis

Diseases [C] » Cardiovascular Diseases [C14] » Vascular Diseases » Vasculitis » Malignant Atrophic Papulosis

Diseases [C] » Skin and Connective Tissue Diseases [C17] » Skin Diseases » Skin Diseases, Vascular » Malignant Atrophic Papulosis

Description

Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.   MeSH

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