Brugada Syndrome D053840

Diseases [C] » Cardiovascular Diseases [C14] » Heart Diseases » Arrhythmias, Cardiac » Brugada Syndrome

Diseases [C] » Cardiovascular Diseases [C14] » Heart Diseases » Cardiac Conduction System Disease » Brugada Syndrome

Description

An autosomal dominant defect of cardiac conduction that is characterized by an abnormal ST-segment in leads V1-V3 on the ELECTROCARDIOGRAM resembling a right BUNDLE-BRANCH BLOCK; high risk of VENTRICULAR TACHYCARDIA; or VENTRICULAR FIBRILLATION; SYNCOPAL EPISODE; and possible sudden death. This syndrome is linked to mutations of gene encoding the cardiac SODIUM CHANNEL alpha subunit.   MeSH

Phase 3 Indicated Drugs (2)


Organization Involved with Phase 4 Indications (1)

Organization Involved with Phase 2 Indications (1)

Organization Involved with Other Experimental Indications (1)

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UMLS Data


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