Erdheim-Chester Disease D031249

Diseases [C] » Hemic and Lymphatic Diseases [C15] » Lymphatic Diseases » Histiocytosis » Histiocytosis, Non-Langerhans-Cell » Erdheim-Chester Disease

Description

A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.   MeSH

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Other Experimental Indicated Drugs (2)


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