Blood Coagulation Disorders, Inherited D025861

Diseases [C] » Hemic and Lymphatic Diseases [C15] » Hematologic Diseases » Blood Coagulation Disorders » Blood Coagulation Disorders, Inherited

Diseases [C] » Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] » Genetic Diseases, Inborn » Blood Coagulation Disorders, Inherited

Description

Hemorrhagic and thrombotic disorders that occur as a consequence of inherited abnormalities in blood coagulation.   MeSH

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Subtype Terms (19)

Activated Protein C Resistance
2 approved drugs

Afibrinogenemia
2 approved drugs

Antithrombin III Deficiency
3 drugs (2 approved, 1 experimental)

Bernard-Soulier Syndrome
 

Factor V Deficiency
 

Factor VII Deficiency
7 drugs (3 approved, 4 experimental)

Factor X Deficiency
1 approved drug

Factor XI Deficiency
1 approved drug

Factor XII Deficiency
 

Factor XIII Deficiency
1 approved drug

Gray Platelet Syndrome
 

Hemophilia A
99 drugs (49 approved, 50 experimental)

Hemophilia B
49 drugs (18 approved, 31 experimental)

Hermanski-Pudlak Syndrome
12 approved drugs

Hypoprothrombinemias
3 approved drugs

Protein C Deficiency
1 approved drug

Thrombasthenia
10 drugs (8 approved, 2 experimental)

von Willebrand Diseases
16 drugs (8 approved, 8 experimental)

Wiskott-Aldrich Syndrome
34 drugs (25 approved, 9 experimental)


Organization Involved with Phase 2 Indications (2)

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UMLS Data


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