Xanthogranuloma, Juvenile D014972

Diseases [C] » Hemic and Lymphatic Diseases [C15] » Lymphatic Diseases » Histiocytosis » Histiocytosis, Non-Langerhans-Cell » Xanthogranuloma, Juvenile

Diseases [C] » Skin and Connective Tissue Diseases [C17] » Skin Diseases » Xanthogranuloma, Juvenile

Description

Benign disorder of infants and children caused by proliferation of HISTIOCYTES, macrophages found in tissues. These histiocytes, usually lipid-laden non-Langerhans cells, form multiple yellow-red nodules most often in the skin, the eye, and sometimes in the viscera. Patients appear to have normal lipid metabolism and are classified as a normolipemic non-Langerhans cell histiocytosis.   MeSH

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