Tyrosine Transaminase D014444

Chemicals and Drugs [D] » Enzymes and Coenzymes [D08] » Enzymes » Transferases » Nitrogenous Group Transferases » Transaminases » Tyrosine Transaminase

Description

An enzyme that catalyzes the conversion of L-TYROSINE and 2-oxoglutarate to 4-hydroxyphenylpyruvate and L-GLUTAMATE. It is a pyridoxal-phosphate protein. L-PHENYLALANINE is hydroxylated to L-tyrosine. The mitochondrial enzyme may be identical with ASPARTATE AMINOTRANSFERASES (EC 2.6.1.1.). Deficiency of this enzyme may cause type II Tyrosinemia (see TYROSINEMIAS). EC 2.6.1.5.   MeSH

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