Purpura, Thrombotic Thrombocytopenic D011697

Related MeSH Hierarchy (5)

Diseases [C] » Hemic and Lymphatic Diseases [C15] » Hematologic Diseases » Blood Coagulation Disorders » Purpura » Purpura, Thrombocytopenic » Purpura, Thrombotic Thrombocytopenic

Diseases [C] » Hemic and Lymphatic Diseases [C15] » Hematologic Diseases » Thrombophilia » Purpura, Thrombotic Thrombocytopenic

Diseases [C] » Pathological Conditions, Signs and Symptoms [C23] » Pathologic Processes » Hemorrhage » Purpura » Purpura, Thrombocytopenic » Purpura, Thrombotic Thrombocytopenic

Diseases [C] » Pathological Conditions, Signs and Symptoms [C23] » Signs and Symptoms » Skin Manifestations » Purpura » Purpura, Thrombocytopenic » Purpura, Thrombotic Thrombocytopenic

Description

An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases.   MeSH

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Phase 4 Indicated Drugs (1)


Organization Involved with Phase 4 Indications (1)

Organization Involved with Phase 1 Indications (2)

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