Pulmonary Alveolar Proteinosis D011649

Diseases [C] » Respiratory Tract Diseases [C08] » Lung Diseases » Pulmonary Alveolar Proteinosis

Description

A PULMONARY ALVEOLI-filling disease, characterized by dense phospholipoproteinaceous deposits in the alveoli, cough, and DYSPNEA. This disease is often related to, congenital or acquired, impaired processing of PULMONARY SURFACTANTS by alveolar macrophages, a process dependent on GRANULOCYTE-MACROPHAGE COLONY-STIMULATING FACTOR.   MeSH

Phase 2 Indicated Drugs (1)

Phase 1 Indicated Drugs (1)


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