Ornithine Carbamoyltransferase D009954

Chemicals and Drugs [D] » Enzymes and Coenzymes [D08] » Enzymes » Transferases » One-Carbon Group Transferases » Carboxyl and Carbamoyl Transferases » Ornithine Carbamoyltransferase

Description

A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3.   MeSH

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