Diseases [C] » Immune System Diseases [C20] » Immunoproliferative Disorders » Lymphoproliferative Disorders » Lymphangiomyoma
Diseases [C] » Neoplasms [C04] » Neoplasms by Histologic Type » Lymphatic Vessel Tumors » Lymphangiomyoma
Diseases [C] » Hemic and Lymphatic Diseases [C15] » Lymphatic Diseases » Lymphoproliferative Disorders » Lymphangiomyoma
Description
A tumorlike condition characterized by SMOOTH MUSCLE and ENDOTHELIUM proliferation of LYMPHATIC VESSELS and LYMPH NODES in the MEDIASTINUM and retroperitoneum, also in the lung. It may be manifested by chylous PLEURAL EFFUSION and ASCITES. MeSH
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Subtype Terms (1)
Lymphangioleiomyomatosis
21 drugs (18 approved, 3 experimental)
Phase 2 Indicated Drugs (1)
Organization Involved with Phase 2 Indications (1)
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UMLS Data
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