Creutzfeldt-Jakob Syndrome D007562

Related MeSH Hierarchy (4)

Diseases [C] » Infections [C01] » Central Nervous System Infections » Prion Diseases » Creutzfeldt-Jakob Syndrome

Diseases [C] » Nervous System Diseases [C10] » Central Nervous System Diseases » Brain Diseases » Dementia » Creutzfeldt-Jakob Syndrome

Psychiatry and Psychology [F] » Mental Disorders [F03] » Neurocognitive Disorders » Dementia » Creutzfeldt-Jakob Syndrome

Description

A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))   MeSH

Phase 2 Indicated Drugs (1)


Organization Involved with Phase 2 Indications (2)

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