Basal Cell Nevus Syndrome D001478

Related MeSH Hierarchy (9)

Diseases [C] » Neoplasms [C04] » Cysts » Bone Cysts » Jaw Cysts » Odontogenic Cysts » Basal Cell Nevus Syndrome

Diseases [C] » Neoplasms [C04] » Neoplasms by Histologic Type » Neoplasms, Glandular and Epithelial » Carcinoma » Carcinoma, Basal Cell » Basal Cell Nevus Syndrome

Diseases [C] » Neoplasms [C04] » Neoplastic Syndromes, Hereditary » Basal Cell Nevus Syndrome

Diseases [C] » Musculoskeletal Diseases [C05] » Bone Diseases » Bone Diseases, Developmental » Basal Cell Nevus Syndrome

Diseases [C] » Musculoskeletal Diseases [C05] » Jaw Diseases » Jaw Cysts » Odontogenic Cysts » Basal Cell Nevus Syndrome

Diseases [C] » Stomatognathic Diseases [C07] » Jaw Diseases » Jaw Cysts » Odontogenic Cysts » Basal Cell Nevus Syndrome

Description

Hereditary disorder consisting of multiple basal cell carcinomas, odontogenic keratocysts, and multiple skeletal defects, e.g., frontal and temporoparietal bossing, bifurcated and splayed ribs, kyphoscoliosis, fusion of vertebrae, and cervicothoracic spina bifida. Genetic transmission is autosomal dominant.   MeSH

Hierarchy View


Phase 1 Indicated Drugs (1)

Other Experimental Indicated Drugs (2)


Organization Involved with Phase 3 Indications (3)

Organization Involved with Phase 1 Indications (4)

Hierarchy Tree View

UMLS Data


YOU AGREE THAT THE INFORMATION PROVIDED ON THIS WEBSITE IS PROVIDED “AS IS”, WITHOUT ANY WARRANTY OF ANY KIND, EXPRESSED OR IMPLIED, INCLUDING WITHOUT LIMITATION WARRANTIES OF MERCHANTABILITY OR FITNESS FOR ANY PARTICULAR PURPOSE, OR NON-INFRINGEMENT OF ANY THIRD-PARTY PATENT, COPYRIGHT, OR ANY OTHER THIRD-PARTY RIGHT. IN NO EVENT SHALL THE CREATORS OF THE WEBSITE OR WASHINGTON UNIVERSITY BE LIABLE FOR ANY DIRECT, INDIRECT, SPECIAL, OR CONSEQUENTIAL DAMAGES ARISING OUT OF OR IN ANY WAY CONNECTED WITH THE WEBSITE, THE USE OF THE WEBSITE, OR THIS AGREEMENT, WHETHER IN BREACH OF CONTRACT, TORT OR OTHERWISE, EVEN IF SUCH PARTY IS ADVISED OF THE POSSIBILITY OF SUCH DAMAGES.