Livedoid Vasculopathy D000090122

Diseases [C] » Cardiovascular Diseases [C14] » Vascular Diseases » Embolism and Thrombosis » Thrombosis » Livedoid Vasculopathy

Diseases [C] » Skin and Connective Tissue Diseases [C17] » Skin Diseases » Skin Diseases, Vascular » Livedoid Vasculopathy

Description

A rare cutaneous thrombotic disease due to occlusion of dermal vessels. It is characterized by purpuric maculae and ulcerations especially during summer which form scars called atrophie blanche. It is more associated with other syndromes (e.g., PROTEIN C DEFICIENCY; HYPERHOMOCYSTEINEMIA). Livedo reticularis with systemic involvement and stroke is SNEDDON SYNDROME.   MeSH

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Subtype Terms (2)

Raynaud Disease
42 drugs (20 approved, 22 experimental)


Phase 1 Indicated Drugs (2)

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