Immunoglobulin G4-Related Disease D000077733

Diseases [C] » Immune System Diseases [C20] » Autoimmune Diseases » Immunoglobulin G4-Related Disease

Description

A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic role. It can affect multiple organs in highly variable presentations, characterized by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS and eventual organ damage.   MeSH

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Phase 3 Indicated Drugs (2)

Phase 1 Indicated Drugs (2)

Other Experimental Indicated Drugs (2)


Organization Involved with Phase 4 Indications (2)

Organization Involved with Phase 3 Indications (2)

Organization Involved with Phase 2 Indications (4)

Organization Involved with Phase 1 Indications (2)

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UMLS Data


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